| CASE REPORT |
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| Year : 2020 | Volume
: 8
| Issue : 4 | Page : 96-98 |
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Bernard–Soulier syndrome and anesthetic management
Manjula Venkatesh Ramsali1, Raj Narasingrao Hadigal1, PG Koshy1, Sirisha Senthil12, P Surender3, V Sarada Devi3
1 Department of Anesthesiology, LVPEI- Hyderabad, Telangana, India
2 Department of Glaucoma, LVPEI- Hyderabad, Telangana, India
3 Department of Anesthesiology, MRMCW-Hyderabad, Telangana, India
Correspondence Address:
Dr. Manjula Venkatesh Ramsali
Department of Anesthesia, LVPEI, Hyderabad, Telangana
India
 Source of Support: None, Conflict of Interest: None
DOI: 10.4103/mjhs.mjhs_16_20
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Bernard–Soulier syndrome (BSS) is a rare autosomal recessive disease with bleeding diathesis due to platelet dysfunction secondary to the absence of the von Willebrand factor receptor on the platelet surface called glycoprotein Ib–V–IX. The deficiency results in prolonged bleeding time and spontaneous bleeds and may be with high risk for anesthesia and surgery. Here, we report a case of BSS coming for trabeculectomy.
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